Skip to main content

Table 1 The practical guideline for performing a comprehensive sequential segmental TTE in the CHD patient

From: A practical guideline for performing a comprehensive transthoracic echocardiogram in the congenital heart disease patient: consensus recommendations from the British Society of Echocardiography

View

(modality)

Anatomy

Measurement ± explanatory note

Image

Subcostal: Transverse / axial plane

(2D & CFD)

Visceral / inferred atrial situs

Indicator @ ~ 3 o’clock

Situs view with IVC, Ab. Ao. and spine in cross section to assess their relative position

Normal (situs solitus): Aorta to left of spine, IVC rightward (± slightly anterior). Rotation and angulation to exhibit long axis of the IVC can be utilised to demonstrate IVC draining into RA

View full size image

Subcostal: Longitudinal / sagittal plane

(2D & CFD)

IVC in long axis

Hepatic vein

Indicator @ ~ 12 o’clock. In situs solitus, slightly rightward tilt for IVC

IVC:

– As detailed by BSE minimum dataset [10]

– Presence, connection, size, RAP estimation [15]

– MM imaging can also be adopted, if perpendicular

Normal: Hepatics return to the IVC, near IVC/RA junction. CFD and PWD in the dominant hepatic vein can be used to inspect for systolic dominance or diastolic reversal (which can infer TR severity and/or restrictive RV physiology)

View full size image

 

Ab. aorta in long axis

Visually assess for pulsatility and for any abnormal flow pattern. From the IVC view, keep indicator at same position and sweep to the left of the patient (in situs solitus) to open Ab. Ao

Note: Depending on probe position celiac trunk/superior mesenteric artery may also be visualised

View full size image

Subcostal: Longitudinal / sagittal plane (PWD)

Ab. aorta

Assess for pulsatility to confirm Ab. Ao. and assess for any abnormal flow pattern. In situs solitus, leftward tilt for Ab. Ao

Normal: Triphasic signal. Some patients may exhibit reduced aortic elastic compliance and loose triphasic profile, but still be considered normal (i.e. older populations, aortic arch repair)

Differential diagnosis:

If continuous pulsatile forward flow, consider;

– Contamination with celiac trunk/superior mesenteric artery flow

– If also blunted/spectral broadening, consider upstream obstruction, i.e. coarctation

If holo-diastolic diastolic flow reversal, likely significant aortic regurgitation, but also consider (particularly if within paediatric practices);

– PDA with significant pulmonary “run-off”

– Aortopulmonary window defect

– Major aortopulmonary collateral arteries

– Unrepaired truncus

– Large Blalock-Taussig shunt

– Duct dependent flow; i.e. AoV atresia, interrupted aortic arch

View full size image

Subcostal: Long axis / coronal plane (2D & CFD)

Heart orientation & position

Indicator @ ~ 3 o’clock

Establish laterality/cardiac position and apex position of the heart

Normal: Left-sided with leftward apex

Entire cardiac morphology, particularly with optimal windows may be appreciated;

– Veno-atrial drainage/connection—Detailed throughout, but if anomalous veno-atrial return (i.e. shunt),

– Atrium morphology—Can be appreciated from multiple windows. Detailed in PSAX window

– Atrioventricular connection and function—Can be appreciated from multiple windows. Detail in A4C description (Fig. 3)

– Ventricular morphology and function—Can be appreciated from multiple windows. Detailed in A4C description. * = septal leaflet chordal attachment of the tricuspid valve

– Shunts—ASD, VSD, PDA

– Ventriculoarterial connection and function

Can be appreciated from multiple windows (subcostal, PSAX, apical);

Normal: Keeping indicator at @ ~ 3 o’clock, tilt anterior to demonstrate outflows sequentially. A sweep stored loop is valuable. Pulmonary outflow is anterior and leftward of the aortic outflow ( →). Branching pattern may help decipher outflow morphology. Other spatial arrangements exist (Fig. 4)

View full size image

View full size image

Pericardium

Pericardial effusion assessment

View full size image

 

Atrial septum

Indicator @ ~ 4/5 o’clock ± anterior tilt

Lengthen IAS. Assess for ASD

Can also visualise RLPV/RUPV and LLPV

Image may require optimising to ensure adequate resolution (frame rate), particularly in adults, in whom the heart is often imaged in the far-field

View full size image

Subcostal: Bicaval Short axis

(2D & CFD)

Atrial septum

RSVC

RAA

Indicator @ 5/6 o’clock

Exhibit veno-atrial drainage/connection

Assess IAS. Assess for ASD

Note: Generally, the recomended image plane (or slightly modified) to interrogate for inferior and superior sinus venous shunt defects. A high right parasternal view with the probe in a super-inferior  orientation can also be adopted. Eustachian valve (IVC) is often seen and if prominent directs flow towards the IAS

Abnormal diastolic flow reversal may be seen with restrictive RV physiology and/or with significant TR severity

May be appreciated on lateral aspect of RA, towards RSVC ostium. Detailed in PSAX window description

View full size image

 

Ventricular morphology

Full heart sweep

Pulmonary outflow

Look for chordal septal attachment of TV (*) to help infer RV morphology and equally MV anatomy & apparatus (this can be confirmed in multiple windows, particularly when there is a sub-optimal subcostal window, i.e. most adult cohorts)

Pulmonic outflow assessment;

Inspect and interrogate for obstruction (sub-, valve, supra-) and/or regurgitation as detailed by BSE minimum dataset [10, 13, 15]

Note: The pulmonary outflow is sometimes best aligned for interrogation from the subcostal window. This is particularly true for the typically anterior located RV-PA conduits, that are often not always easily identified

Can assess full cardiac morphology, as previously detailed. Sweep laterally from bicaval to LV apex (akin to PSAX window)

View full size image

 

MV/LAVV

Detailed in PSAX window. Qualitative assessment of leaflet morphology, thickness, excursion, regurgitation, chordae and papillary morphology/apparatus abnormalities

Normal MV: The AMVL is parallel to the ventricular septum as depicted (versus perpendicular orientation to the ventricular septum for LAVV anatomy)

View full size image

Subcostal:

RV inflow/outflow

(2D & CFD)

RAO view

AKA

“ToF View”

AoV, IAS, RA, TV, RV, RVOT, PA, MPA & PA branches

Indicator @ 1 o’clock. A similar RV inflow/outflow window ( →) can be replicated from a modified apical RV 3 chamber window

Offset between the AoV and PV can often be well appreciated, with PV morphology being superior

Assess for VSD, abnormality of outlet septum, RVOT obstruction and/or double chambered RV anatomy;                

Normal (sub-pulmonary): The right ventricle—pulmonary artery junction has a complete circumferential muscular outlet-septum boundary, resulting in discontinuity between the tricuspid valve and pulmonary outflow. The left ventricle—aortic outflow does not, which results in aortomitral continuity

View full size image

Apical:

A4C

(2D & CFD)

Full heart sweep

State sweep direction:

Can assess full cardiac morphology, as previously detailed

Note: Although IAS mobility and competence can be appreciated, caution must be adhered to with regards to potential ASD interrogation, sizing and shunt direction due to lateral resolution “drop out” artefact. Assess for ASD; A modified A4C where the septum is orientated more perpendicular will help minimise error.

* = moderator band

 →  = atrioventricular valve offset

View full size image

Pulmonary veins:

RLPV/RUPV & LLPV

Pulmonary vein identification;

As detailed by BSE minimum dataset [10, 15]

 RLPV is most likely seen when adjacent to the IAS in A4C with RUPV more likely to be visualised when more anteriorly tilted

LLPV is generally well appreciated from A4C

Note: Identification and interrogation for pulmonary veins is important with respect to;

–Anomalous drainage/connection

–Isolated obstruction

–Atrioventricular valve regurgitation

–Diastolic function

View full size image

View full size image

A4C

(PWD/CWD)

Pulmonary veins

Pulmonary vein interrogation;

A higher sweep speed (i.e. > 75 mm/s) will facilitate greater accuracy of atrial reversal duration measurement. As detailed by BSE minimum dataset [10, 15]

View full size image

 

Atrio-ventricular connection & ventricular morphology

The atrioventricular valve directly correlates to the morphological ventricle;

– Left ventricle = MV: Inserts further from apex

– Right ventricle = TV: Inserts closer to the apex (A)

– Atrioventricular valve offset: If offset is reversed (B), the TV is abnormally apically inserted (Ebsteins: > 8 mm/m2, C), or not offset (D), question underlying atrioventricular anatomy (Fig. 3)

View full size image

Morphology can then further be interrogated from the following;

– Leaflet morphology (in absence of common atrioventricular valve):

 TV: Trileaflet triangular orifice with septal leaflet attachment into the ventricular myocardium

 MV: Bileaflet elliptical orifice with typically two distinct papillary muscles inserted antero-laterally and postero-medially (SAX and A2C windows)

– Moderator band: Increases likelihood of RV morphology

– Wall smoothness: RV more likely to have a courser septal surface with apical trabeculation versus a smooth walled LV

– Ventricular shape: RV is crescentic versus cone-like LV appearance

View full size image

A4C

(2D & CFD)

MV/LAVV

Caution must be adhered to when assessing systemic TVs or LAVVs with respect to BSE adult quantification data, as it will not be directly applicable

Systemic regurgitation assessment;

– If MV, as detailed by BSE guidelines [11, 15]

–Dominant MV scallops in A4C: A3/A2 & P1

View full size image

 

Left atrium

Systemic stenosis assessment;

– As detailed by BSE guidelines [11, 15]

LA size (end systolic volume): Biplane

– As detailed by BSE minimum dataset [10, 15]

View full size image

 

MV/LAVV

Caution must be adhered to when quantifying regurgitation and/or stenosis in the presence of intracardiac shunts

Systemic regurgitation assessment;

As detailed by BSE guidelines [11, 15]

View full size image

  

Systemic stenosis asessment;

As detailed by BSE guidelines [11, 15]

View full size image

A4C

(PWD)

MV/LAVV

Caution must be adhered to when quantifying inflow with respect to atrial switch biventricular repair anatomies or univentricular physiology

Systemic inflow;

As detailed by BSE minimum dataset [10, 11, 15]

View full size image

A4C

(TDI/MM)

Basal lateral and basal septal annulus

Caution must be adhered to when quantifying TDI with respect to atrial switch biventricular repair anatomies or univentricular physiology

Systemic systolic and diastolic assessment;

-As detailed by BSE minimum dataset [10, 11, 15]

Note: Limited utility when RWMA are present or expected (i.e. VSD patch, atrioventricular valve repair/replacement)

View full size image

 

Lateral annulus

MAPSE

As detailed by BSE minimum dataset [10, 15]

View full size image

A5C

(2D & CFD)

Outflow/root

Ventriculoarterial connection and function;

Tilt anterior to demonstrate outflows sequentially. A sweep stored loop may be of value

Normal: Pulmonary valve/outflow is anterior and leftward of the aortic valve/outflow. Branching pattern may help decipher outflow morphology. Spatial orientation of the ventriculoarterial connections can be appreciated (Fig. 4)

Systemic outflow assessment;

– Inspect and interrogate for obstruction (sub-, valve, supra-) and/or regurgitation as detailed by BSE minimum dataset [10, 12]

Normal: Aortomitral continuity as sub-pulmonary outlet septum morphology

In atrioventricular septal defect anatomies, there is unwedging of the aorta with absence of atrioventricular—ventriculoarterial continuity. Aortomitral discontinuity will also be noted with respect to systemic RV physiology

View full size image

 

Coronaries

In addition to PSAX window, coronary ostia and their course can sometimes be appreciated when interrogating the aortic outflow with further anterior modified angulations ( )

View full size image

A5C

(PWD/CWD)

Outflow/root

Systemic outflow assessment;

-Inspect and interrogate for obstruction (sub-, valve, supra-) and/or regurgitation as detailed by BSE minimum dataset [10, 12, 15]

Note: Supra-valvular outflow obstructions are often well visualised and quantified from suprasternal and right parasternal windows

View full size image

A4C

2D Zoom

Left ventricle

Systemic LV assessment;

As detailed by BSE minimum dataset [10, 15]

–A4C LV ( →):

 IS: Infero-septum wall

 AL: Antero-lateral wall

Measures should be indexed to BSA or Z-scored (if paediatrics)

View full size image

A2C

(2D, CFD, PWD, CWD), 2D Zoom

Left ventricle

Left atrium

Systemic LV assessment;

As detailed by BSE minimum dataset [10, 15]

–A2C LV ( →):

 I: Inferior wall

 A: Anterior wall

LA size (end systolic volume); Biplane

– As detailed by BSE minimum dataset [10, 15]

View full size image

MV/LAVV

If MV: P3/A2 (enface)/P1. Assess for stenosis and/or regurgitation as detailed by BSE guidelines [10, 11, 15]. Assessment of papillary muscle number and location with modified angulations

Note: X-plane enface imaging or 3D helpful when interrogating anatomy [11], especially if LAVV

 

Pulmonary veins

LUPV is seen adjacent to LAA, separated by the coumadin ridge.

View full size image

Coronary sinus

RLPV/RUPV may also be appreciated with modified angulation

CS may also be appreciated enface, adjacent to the basal inferior wall, within the atrioventricular groove

Ab. aorta

Further posterior angulation will demonstrate the Ab. Ao. in its long axis

A3C

(2D, CFD, PWD, CWD),

2D Zoom

Left ventricle

Systemic LV assessment;

– As detailed by BSE minimum dataset [10]

– A3C LV ( →):

 IL: Infero-lateral wall

 AS: Antero-septum wall

View full size image

 

MV/LAVV

Outflow/root

IF MV: Likely A2/P2. Assess for stenosis and/or regurgitation as detailed by BSE guidelines [10, 11, 15]

Systemic outflow assessment;

Inspect and interrogate for obstruction (sub-, valve, supra-) and/or regurgitation as detailed by BSE minimum dataset [10, 12, 15]

A4C RV

(2D & CFD, MM, TDI)

Right ventricle

RA

Subpulmonic RV assessment;

As detailed by BSE minimum dataset [10, 14, 15]

- If RV: Lateral RV “free” wall

Note: Systemic RV assessment is largely qualitative, with measurement parameters adopted for longitudinal follow-up comparison

RA size (end systolic area);

-As detailed by BSE minimum dataset [10, 15]

View full size image

  

Obtain a RV focussed view to allow entire RV free wall to be interrogated and RV dimensions to be measured from. As detailed by BSE minimum dataset [10, 14, 15]

View full size image

 

TV/RAVV

Caution must be adhered to when assessing subpulmonic MVs or RAVVs with respect to BSE adult TV quantification data, as it will not be directly applicable

Subpulmonic TV inflow stenosis/regurgitation;

– Assess as detailed by BSE guidelines [13, 15]

– If TV: Likely anterior (A) & septal (S) leaflets

– Posterior (P) leaflet if CS angulated in view

Note: X-plane enface imaging or 3D helpful when interrogating anatomy [13]

View full size image

 

Coronary sinus

With posterior angulation, CS can be appreciated, draining back into the RA within the left posterior atrioventricular groove. In LSVC anatomy, a dilated CS is often seen (right example). Note: The LSVC is a left atrium morphological structure

If CS is unroofed/fenestrated, thus shunting

physiologically, haemodynamically will act as an ASD with left to right shunting

View full size image

RSVC

Sometimes noted very anterior

 

RAA

Broad based orifice and anterior. Christa terminalis (prominent muscle bar separating RSVC—RAA) may be seen

View full size image

 

Eustachian valve

 →  = Eustachian valve (EV)/ridge can sometimes be seen and if may be noted to change inflow profile. It is typically a relatively rigid structure, inserting more caudally (infero-posterior), but can also be mobile and fenestrated. It is different to the Chiari network due to its insertion point, which inserts superior-anterior

This is a normal anatomical variant. Possible erroneous pathologic interpretation typically includes mass lesion or Cor triatriatum dexter

View full size image

Modified apical RV 3 chamber

Inflow/outflow

(2D & CFD)

RA, TV, RV, RVOT, PA, MPA & PA branches

Anterior probe tilt with indicator rotated between 12–2 o’clock, akin to the subcostal RV inflow-outflow window ( →)

Depending on rotation of probe, aortic valve may be seen enface [13], if TV:

– Adjacent to AoV and no septum—anterior (A) TV leaflet

– Liver noted/inferior RV wall—posterior (P) TV leaflet

Offset between the AoV and PV can then be appreciated with PV morphology being superior

Assess for abnormality of tricuspid valve (i.e. Ebstein’s), VSD, outlet septum, RVOT obstruction and/or double chambered RV anatomy

View full size image

A4C RV

(PWD/CWD)

TV/RAVV

Caution must be adhered to when quantifying regurgitation and/or stenosis in the presence of intracardiac shunts

Est. RVSP = TR Vmax + RAP

– If no valvular stenosis, regurgitation, or downstream stenosis (i.e. branch pulmonary arteries), use as surrogate for PASP

Note: RVSP/PASP will be underestimated with severe/free TR and should not be relied upon

View full size image

  

Subpulmonic TV stenosis/regurgitation;

– Assess as detailed by BSE guidelines [10, 13, 15]

View full size image

Modified A4C PV

(2D, CFD, PWD, CWD),

Outflow/root

Ventriculoarterial connection and function;

Tilt further anterior than A5C to demonstrate pulmonary outflow, if required. In some patients, branch pulmonary arteries can also be appreciated

Typically, a rib-space higher with lateral or medial modification will optimise this pulmonary outflow window, which can be fully examined

Normal: Pulmonary valve/outflow is anterior and leftward of the aortic valve/outflow. Branching pattern may help decipher outflow morphology. Spatial orientation of the ventriculoarterial connections can be appreciated (Fig. 4)

View full size image

Left PLAX

(2D & CFD)

Full heart sweep

State sweep direction: “VSD sweep”

Can assess full cardiac morphology, as detailed in previous sweep descriptions

Note: Parasternal imaging often exhibits best VSD visualisation and quantification

Ventriculoarterial connection;

Pulmonary valve/outflow is anterior and leftward of the aortic valve/outflow. Branching pattern may help decipher outflow morphology. Spatial orientation of the ventriculoarterial connections can be appreciated (Fig. 4)

View full size image

Left PLAX

(2D & CFD)

Pericardial/pleural space

MV/LAVV

LA

Increase scan depth

Assess annulus, mobility, thickness, calcification, supra or sub valvular apparatus

Systemic stenosis/regurgitation assessment;

– If MV, measures as detailed by BSE guidelines [10, 11, 15]

  MV scallops usually demonstrated are;

  Standard PLAX: A2 & P2

  Modified RV inflow tilt: A3 & P3

  Modified RV outflow tilt: A1 & P1

  MM may help demonstrate pathology

Note: X-plane enface imaging or 3D helpful when interrogating anatomy [11], especially if LAVV

View full size image

Left ventricle

Systemic LV assessment;

– As detailed by BSE minimum dataset [10, 15]

– PLAX LV ( →):

   IL: Infero-lateral wall

  AS: Antero-septum wall

View full size image

 

Coronary sinus

CS (enface): Posterior within left posterior atrioventricular groove. If dilated, a high index of suspicion is warranted for persistent LSVC anatomy

Prox. RVOT

Note: Ab. Ao. is seen posterior, outside of the pericardium

As detailed by BSE minimum dataset [10, 15]

If RV: Anterior RV wall

 

Pulmonary veins

LLPV: Adjacent to inferolateral LV annulus

Other veins may also be interrogated with modified imaging windows

View full size image

Left PLAX: 2D Zoom

(2D & CFD)

LVOT/outflow

Systemic outflow assessment;

– Inspect and interrogate for obstruction (sub-, valve, supra-) and/or regurgitation as detailed by BSE minimum dataset [10, 12, 15]

Normal: If trileaflet aortic valve: right coronary cusp (RCC) is seen anteriorly, extending from ventricular septal aspect. Depending on tilt, either non (NCC)- or left- coronary cusp may been seen posteriorly with continuity to the AMVL, due to normal outlet (sub-pulmonary) septum morphology

* = sub-aortic ridge

View full size image

 

Root

Aortic root appearance and dimensions. Moving up a rib-space/superiorly will often optimise view

Outflow measurements should be made as detailed by BSE minimum dataset, documenting method of quantification (i.e. edge: inner to inner [i2i] or leading to leading [L2L] and timing: end diastole or end systole) alongside absolute values;

– BSE Height index (mm/m)—end diastole [15]

– Z-score (label which dataset)

– BSA correction (cm/m2): i.e. Turners

View full size image

 

RCA

RCA ostium may be appreciated arising from the sinus. The RCA typically courses rightward (in PLAX) behind the pulmonary artery and below the right atrial appendage along the right atrioventricular groove

Note: High take-off (superior to sinus) may also be appreciated as a normal variant

View full size image

Left PLAX: RV inflow

(2D & CFD)

RA

TV/RAVV

Atrial septum

Inflow stenosis/regurgitation;

– As detailed by BSE minimum dataset [10, 15]

– Note: A PMVSD jet may contaminate TR

The beam tilt will dictate which TV leaflets are likely visualised [10, 13, 15], if TV;

– Anterior (A) and posterior (P) leaflets when LV/ventricular septum and CS are no longer visualised

– Anterior and septal (S) leaflets when ventricular septum and CS ostia to RA noted

Note: X-plane enface imaging or 3D helpful when interrogating anatomy, especially if RAVV

A modified “RV inflow” with more lateral and caudal probe positioning (i.e. a rib space lower) can exhibit IAS. Assess for ASD

View full size image

 

Right ventricle

IVC, CS

RV size and function [10, 13]

When LV/ventricular septum is no longer visualised, RV inferior wall is seen adjacent to diaphragm/liver with contralateral RV anterior wall noted

If RV:

 A: Anterior RV wall

 I: Inferior RV wall

Can be identified with modified inflow tilt. Remnant Thebesian valve from the CS (*), Eustachian valve from the IVC (#) and/or Chiari network (mobile net-like structure) may be identified and noted to change the inflow profile. It is typically a relatively rigid structure, inserting more caudally (infero-posterior), but can also be mobile and fenestrated. It is a normal anatomical variant. Possible erroneous pathologic interpretation typically includes mass lesion or Cor triatriatum dexter

View full size image

 

TV/RAVV

Inflow stenosis/regurgitation;

– As detailed by BSE minimum dataset [10, 13, 15]

– Note: a PMVSD jet may contaminate TR

View full size image

Left PLAX: RV outflow

(2D & CFD)

Distal RVOT

PV, MPA & PAs

Tilt superior and centralise

Pulmonic outflow assessment;

– Inspect and interrogate for obstruction (sub-, valve, supra-) and/or regurgitation as detailed by BSE minimum dataset [10, 13, 15]

Ventriculoarterial connection;

Pulmonary valve/outflow is anterior and leftward of the aortic valve/outflow. Branching pattern may help decipher outflow morphology. Spatial orientation of the ventriculoarterial connections can be appreciated (Fig. 4)

Notes:

–LPA is left-sided in PLAX

–PDA can sometimes be examined here if Ductal view is non-obtainable

View full size image

Left PLAX: RV outflow

(PWD/CWD)

Distal RVOT

PV outflow, MPA & PAs

Pulmonic outflow assessment;

– Inspect and interrogate for obstruction (sub-, valve, supra-) and/or regurgitation as detailed by BSE minimum dataset [10, 13, 15]

View full size image

Can also do in PSAX

Measures;

Sub-valvular PWD (Vmax, VTI, SV). Use PWD “step-through” if suspected sub- or supra-valvular obstruction

– Sub-pulmonic obstruction CWD (Vmax, VTI, mean PG)

  

– Sub-pulmonic regurgitation CWD (density, contour, PHT, PR Vmax, PR Vend, PR index)

– Est. Mean PAP: PR Vmax + RAP

– Est. End diastolic PAP: PR Vend + RAP

– If notching is noted: likely raised pulmonary pressures

Note: Severe PR is likely if flow reversal is noted on CFD and Doppler within the branch PAs

View full size image

Left PSAX:

(2D & CFD)

Full heart sweep

Pericardial / pleural space

State sweep direction: “VSD sweep”

Can assess full cardiac morphology, as detailed in previous sweep descriptions

In order to maintain adequate frame rate, it is recommended CFD “box-size” is reduced to cover myocardial lateral and septal aspects individually when inspecting for VSDs

Note: Parasternal imaging often exhibits best VSD visualisation and quantification

Increase scan depth

View full size image

Left PSAX: AoV level

(2D & CFD)

Aortic valve

RVOT, PA, MPA & PA

Qualitative assessment of cusp morphology and function

– As detailed by BSE minimum dataset [10]

Spatial orientation of the ventriculoarterial connections can be appreciated (Fig. 4)

Normal: Pulmonary valve/outflow is anterior and leftward of the aortic valve/outflow. Branching pattern may help decipher outflow morphology. RV inflow-outflow demonstrated ( →)

View full size image

Coronary origins

Coronaries in almost all cases arise from the aortic sinuses facing the pulmonary valve. The non-facing sinus/non-coronary cusp is always the cusp adjacent to the IAS

Use coronary specific imaging settings (i.e. high frequency, low compress, increased 2D gain, zoom). If normal, they arise slightly superior (i.e. up a rib-space) to the respective cusps. By TTE;

– LCA: indicator ~ 2/3 o’clock (sometimes further clockwise rotation is warranted) with ostium originating typically at 3 o’clock and courses rightward (in PSAX) before bifurcating into left anterior descending (upward in PSAX: #) and left circumflex arteries (downward in PSAX: *)

– RCA: indicator ~ 1 o’clock with ostium originating typically at 11 o’clock and coursing leftward (in PSAX)

View full size image

For increased diagnostic accuracy (i.e. to rule out erroneous pericardial fold/coronary vein), origins can be demonstrated with CFD (reduced Nyquist scale), exhibiting predominantly diastolic antegrade flow in the structurally normal heart without known occlusive coronary artery disease

View full size image

Modified left PSAX: AoV level

(2D & CFD)

Atrial septum

RA

TV/RAVV

A focused image is recommended. Assess for ASD

Inflow stenosis/regurgitation;

– As detailed by BSE minimum dataset [10, 13, 15]

– Note: A PMVSD jet may contaminate TR

If TV: Leaflet cusps will vary depending on level of valve interrogation [13]

Note: X-plane enface imaging or 3D helpful when interrogating anatomy [13], especially if RAVV

View full size image

 

Atrium morphology

LAA

Atrial arrangement is largely inferred from the abdominal visceral situs as direct visualisation of both atrial appendages (particularly RAA) is challenging by TTE. Therefore, site of the appendages is mostly complimentary (Fig. 1)

Following PSAX branch PA bifurcation image optimisation, which is typically a rib-space higher than standard, tilt posterior from RPA to “open” LAA and respective pulmonary veins

LAA: Typically, narrow orifice and posterior (modified PSAX or A2C), finger-like appearance by TTE

View full size image

 

RAA

Typically, a rib-space higher with medial probe positioning for right atrial appendage. It lies near RSVC insertion

RAA: typically, triangular with broad based orifice and anterior (modified PSAX), Christa terminalis (prominent muscle bar separating RSVC—RAA) may be seen. Pectinate muscles are course and extend towards the tricuspid valve

View full size image

 

LSVC

If present, further modified imaging planes (indicator towards 1 o’clock) can visualise the LSVC in its long axis. Typically, a persistent LSVC passes anterior to the LPA before coursing infero-posterior along the left atrioventricular groove into the coronary sinus before draining into the right atrium. In adults, the proximal course of the LSVC is best appreciated from the SSN window

View full size image

Modified left PSAX:AoV level

(2D & CFD)

RVOT, PV outflow, MPA & PAs

Pulmonic outflow assessment;

Inspect and interrogate for obstruction (sub-, valve, supra-) and/or regurgitation as detailed by BSE minimum dataset [10, 13, 15]

Notes:

– A rib-space higher may aid branch PA bifurcation optimisation (right pane)

– LPA is right sided in PSAX indicator projection

– Large margins of error can exist with respect to RVOT/outflow dimensions and the rib space the probe is positioned within

View full size image

 

Pulmonary veins

By TTE, it is generally accepted within CHD that at least 3 pulmonary veins are observed returning to the LA (from any imaging plane)

LAA (bi-directional CFD) & LUPV posterior, when in PSAX window

View full size image

  

LLPV—red

View full size image

  

RLPV—red

RUPV—blue (often difficult to appreciate in this view)

Note: Pulmonary veins can be appreciated from numerous windows. It may also be possible in some populations to appreciate pulmonary veins via the SSN “Crab" view

View full size image

 

Eustachian valve/Chiari network

Eustachian valve (#) can sometimes be seen and may be noted to change inflow profile. It is typically a relatively rigid structure, inserting more caudally (infero-posterior), but can also be mobile and fenestrated. It is different to the Chiari network (= ) due to its insertion point, which inserts superior-anterior

This is a normal anatomical variant. Possible erroneous pathologic interpretation typically includes mass lesion or Cor triatriatum dexter

View full size image

Modified high “ductal view”

(2D, CFD, CWD)             

High left parasternal longitudinal / sagittal plane

Proximal LPA with isthmus/Desc. aorta in long axis

Sweep to assess for PDA. Indicator towards 12/1 o’clock, at least one rib space higher and typically immediately adjacent to the left side of the sternum

Often patient needs to be in an extreme left lateral decubitus position to optimise

View full size image

Left PSAX: Basal level

(2D & CFD)

MV/LAVV

TV/RAVV

Qualitative assessment of leaflet morphology, thickness, excursion, regurgitation

* = Anterolateral commissure

# = Posteromedial commissure

Note: Xplane or 3D imaging is useful to appreciate atrioventricular anatomy in both SAX and the corresponding LAX projection [11], especially if LAVV/RAVV

View full size image

Left ventricle

Qualitative assessment of radial function/RWMA (n: 6)

Right ventricle

Qualitative assessment of radial function. If RV;

A: Anterior RV wall

I: Inferior RV wall

L: Lateral RV “free” wall

Left PSAX: Mid-level

(2D & CFD)

Left ventricle

Right ventricle

MV/LAVV

TV/RAVV

Qualitative assessment of radial function/RWMA (n: 6)

Can assess septal curvature loading in systole (pressure) and diastole (volume). Can utilise Eccentricity index (just below level of MV leaflets), ensuring correct measurement alignment

Normal Eccentric index: < 1.2

Qualitative assessment of radial function

A: Anterior RV wall

I: Inferior RV wall

L: Lateral RV “free” wall

Assess chordae and papillary morphology/apparatus abnormalities

* = Lateral papillary muscle

# = Medial papillary muscle

View full size image

Left PSAX: Apical level

(2D & CFD)

Left ventricle

Qualitative assessment of radial function/RWMA (n: 4)

View full size image

SSN long axis

(2D & CFD)

Aortic arch

Have good head tilt/shoulders raised. This standard window should be modified to appreciate optimised vessel calibre, including;

– Asc. Ao

– Transverse Arch (between BCA/IA & LCCA)

– Desc. Ao

– RPA (enface)

– Head and neck vessels (BCA/IA, LCCA, LSA)

Abnormal colour patterns. Assess for coarctation, PDA or anomalous pulmonary vertical vein                         

Note: A right sided aortic arch will require a degree of rightward angulation to appreciate Desc. Ao., and LPA in their respective long axis projections

View full size image

SSN long axis

(PWD/CWD)

Aortic arch

Individual vessels can be interrogated by Doppler (including Pedof probe if warranted);

– Distal Asc. Ao: CWD

– Desc. Ao.: PWD (stepdown if warranted) & CWD

Normal: Triphasic signal. Some patients may exhibit reduced elastic compliance and loose triphasic profile, but still be considered normal

–Head and neck vessels (BCA/IA, LCCA, LSA)

If there is evidence of continuous antegrade diastolic forward flow (“diastolic tail”), likely to reflect a degree of narrowing/coarctation of the aorta

View full size image

  

If holo-diastolic diastolic flow reversal, likely significant aortic regurgitation, but consider;

– PDA with significant pulmonary “run-off”

– Aortopulmonary window defect

– Major aortopulmonary collateral arteries

– Unrepaired truncus

– Large Blalock-Taussig shunt

– Duct dependent flow;

   i.e. AoV atresia, interrupted aortic arch

View full size image

Leftward modified SSN long axis

(2D, CFD, PWD, CWD)

LPA

Innominate vein

Sweep left lateral to open LPA in long axis (LPA is anterior to Desc. Ao.), assess for obstruction, flow reversal and/or use if PDA and if LPA not well seen previously in other imaging windows (typically adult cohorts)

Note: In the presence of valvular or supravalvular pulmonary obstruction, mixed/residual flow acceleration is often exhibited in the LPA, which itself may be of normal calibre

Often seen in many SSN views but may run retro-aortic as a normal variant

View full size image

 

LSVC

If present, further modified imaging planes can visualise the LSVC in its long axis. Typically, a persistent LSVC passes anterior to the LPA before coursing infero-posterior along the left atrioventricular groove into the coronary sinus before draining into the right atrium

Sometimes bilateral SVCs anatomies will have a bridging vein, that is often difficult to appreciate by TTE

View full size image

SSN short axis

(2D & CFD)

Arch sidedness

Indicator at 3 o’clock. Further rotation of indicator to 4/5 o’clock can help illustrate the BCA/IA in its long axis projection

Sweep superior/anterior and follow first head and neck vessel and follow branching pattern

Note: First arch vessel is typically BCA/IA and arch sidedness is typically contralateral to its direction

Normal: Left sided aortic arch: BCA/IA is rightward and bifurcates

View full size image

  

Right sided aortic arch: BCA/IA is leftward and in normal head and neck vessel arrangement will also bifurcate

Note: Left and right aortic arch refers to which side the bronchus/trachea are crossed by the aortic arch, not which side of the midline the aortic root or Desc. Ao. takes

There are many variations of head and neck vessel arrangement. Of which, TTE is often sub-optimal to provide detailed diagnosis

View full size image

SSN short axis

(2D & CFD)

RPA

Venous anatomy

Assess calibre and flow pattern, if not assessed earlier in study. Optimise Doppler angle. The more perpendicular, the less reliable due to angle of incidence principle

Long axis Innominate vein to RSVC

Normal: Innominate vein (AKA brachiocephalic vein) is typically anterior to the Asc. Ao. and drains to the RSVC

View full size image

SSN short axis: “Crab view”

(2D & CFD)

Pulmonary veins:

LLPV

LUPV

RLPV

RUPV

Pulmonary veins can be appreciated from numerous windows. It is largely accepted that “crab view” in adult populations is often sub-optimal

Normal;

LLPV—red

LUPV—blue

View full size image

  

Normal;

RLPV—red

RUPV—blue

View full size image

High right parasternal: Longitudinal view

(2D, CFD, PWD, CWD)

Outflow/aortic root

Indicator at ~ 11–1 o’clock. Ascending aortic vessel can be interrogated (Pedof probe is recommended) for obstruction. Often useful in interrogating any valvular/supra-valvular obstruction with eccentric forward flow jets that are often difficult to align optimally elsewhere

View full size image

IAS, RSVC, IVC

Indicator at ~ 12 o’clock

Often patient needs to be in the right-sided decubitus position

View full size image

Supraclavicular view

(2D, CFD, PWD, CWD)

SVC

Indicator at ~ 12 o’clock

A right supraclavicular view may be used where necessary (i.e. assessment in Fontan circuit: RSVC Glenn ± distal conduit anastomosis sites). The same interrogation may also be performed in the left supraclavicular view for left SVC anatomy

In adult populations, RSVC is not always best appreciated from the SSN SAX imaging, and this window can be adopted

View full size image