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Three-dimensional echocardiography of congenital abnormalities of the left atrioventricular valve

Abstract

Congenital abnormalities of the left atrioventricular (AV) valve are a significant diagnostic challenge. Traditionally, reliance has been placed on two-dimensional echocardiographic (2DE) imaging to guide recognition of the specific morphological features. Real-time 3DE can provide unique views of the left AV valve with the potential to improve understanding of valve morphology and function to facilitate surgical planning. This review illustrates the features of congenital abnormalities of the left AV valve assessed by 3DE. The similarities and differences in morphology between different lesions are described, both with respect to the valve itself and supporting chordal apparatus. The potential advantages as well as limitations of this technique in clinical practice are outlined.

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This review did not receive any specific grant from any funding agency in the public, commercial or not-for-profit sector.

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Correspondence to John Simpson MD FRCP FESC.

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Rice, K., Simpson, J. Three-dimensional echocardiography of congenital abnormalities of the left atrioventricular valve. Echo Res Pract 2, R13–R24 (2015). https://doi.org/10.1530/ERP-15-0003

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  • DOI: https://doi.org/10.1530/ERP-15-0003

Key Words

  • mitral valve
  • left atrioventricular valve
  • three-dimensional echocardiography
  • congenital heart disease
  • atrioventricular septal defect
  • congenital mitral valve lesions