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Atrialised right ventricular myxoma in a patient with Ebstein’s anomaly

Echo Research & Practice volume 5, pages K23–K27 (2018)Cite this article

Summary

Ebstein’s anomaly is a rare entity affecting around 1 in 200,000 live births and accounts for less than 1% of congenital heart diseases. Ebstein’s anomaly with an associated right-sided myxoma is extremely rare, with only one other case report found in the literature. Previous reports have also noted cases of Ebstein’s anomaly associated with left-sided myxomas. We describe a female patient with, to our knowledge, the first case of a histopathologically confirmed right ventricular myxoma in the setting of Ebstein’s anomaly.

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Authors and Affiliations

  1. Division of Cardiology, Department of Medicine, University of Stellenbosch, Cape Town, South Africa

    T-J. John, H. W. Snyman & J. Janson

  2. Department of Cardiothoracic Surgery, University of Stellenbosch, Cape Town, South Africa

    A. J. K. Pecoraro

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  1. T-J. John
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  2. H. W. Snyman
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  3. J. Janson
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  4. A. J. K. Pecoraro
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Correspondence to T-J. John.

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John, TJ., Snyman, H.W., Janson, J. et al. Atrialised right ventricular myxoma in a patient with Ebstein’s anomaly. Echo Res Pract 5, K23–K27 (2018). https://doi.org/10.1530/ERP-17-0065

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  • DOI: https://doi.org/10.1530/ERP-17-0065

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Echo Research & Practice

ISSN: 2055-0464

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